Sprengel's deformity
From Wikipedia, the free encyclopedia
Sprengel's deformity Classification and external resources |
|
ICD-10 | Q74.0 |
---|---|
ICD-9 | 755.52 |
OMIM | 184400 |
DiseasesDB | 31521 |
eMedicine | orthoped/445 |
Sprengel's deformity is a relatively rare and congenital skeletal abnormality where a person has one shoulder blade that sits higher on the back than the other.
[edit] Presentation
The scapula is small and rotated so that its inferior edge points toward the spine. There is a high correlation between Sprengel's deformity and the Klippel-Feil syndrome.
Sometimes a a bony connection is present between the elevated scapula and one of the cervical vertebrae, usually C5 or C6. This connection is known as the omovertebral bone.
[edit] Eponym
It is named for Otto Sprengel.[1][2]
[edit] References
- ^ synd/2450 at Who Named It
- ^ O. K. Sprengel. Die angeborene Verschiebung des Schulterblattes nach oben. Archiv für klinische Chirurgie, Berlin, 1891, 42: 545-549.