Gonadal dysgenesis
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Gonadal dysgenesis Classification and external resources |
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ICD-10 | Q99.1 |
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ICD-9 | 758.6 |
MeSH | D006059 |
Gonadal dysgenesis generally refers to a condition where gonadal development is abnormal, often only presenting streaks of connective tissue: so-called streak gonads.
[edit] Causes
The condition may be due to:
- Turner syndrome, and its variations (i.e. mosaicism)
- XX gonadal dysgenesis, also pure gonadal dysgenesis, 46, XX
- Swyer syndrome, also pure gonadal dysgenesis, 46, XY
- Perrault syndrome
- Mixed gonadal dysgenesis
- Endocrine disruptors
[edit] Presentation
It is one of the causes of intersexuality, because the genitalia are determined to be neither exclusively male nor female.
[edit] See also
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