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Achard-Thiers syndrome - Wikipedia, the free encyclopedia

Achard-Thiers syndrome

From Wikipedia, the free encyclopedia

Achard-Thiers syndrome
Classification and external resources
ICD-10 E25.9
ICD-9 255.2
DiseasesDB 33820

Achard-Thiers syndrome combines the features of Adrenogenital syndrome and Cushing syndrome. It is also known as diabetic-bearded woman syndrome (diabète des femmes à barbe).

The disease is named for Emile Achard and Joseph Thiers.

[edit] Clinical features

Achard-Thiers syndrome affects mostly postmenopausal women and comprises diabetes mellitus, deep voice, hirsutism or hypertrichosis, clitoral hypertrophy and adrenal cortical hyperplasia or adenoma. Patients often also have amenorrhoea, hypertension and osteoporosis.

[edit] References

Languages


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